{"id":2837,"date":"2022-06-01T09:56:24","date_gmt":"2022-06-01T07:56:24","guid":{"rendered":"https:\/\/www.progettomitofusina2.com\/welcome-all\/%d0%b0%d1%81%d0%be%d1%86%d0%b8%d0%b0%d1%86%d0%b8%d1%8f%d1%82%d0%b0-%d0%bf%d1%80%d0%be%d0%b5%d0%ba%d1%82-mitofusina-2-onlus\/"},"modified":"2022-06-13T14:37:41","modified_gmt":"2022-06-13T12:37:41","slug":"%d0%b0%d1%81%d0%be%d1%86%d0%b8%d0%b0%d1%86%d0%b8%d1%8f%d1%82%d0%b0-%d0%bf%d1%80%d0%be%d0%b5%d0%ba%d1%82-mitofusina-2-onlus","status":"publish","type":"page","link":"https:\/\/www.progettomitofusina2.com\/en\/welcome-all\/%d0%b0%d1%81%d0%be%d1%86%d0%b8%d0%b0%d1%86%d0%b8%d1%8f%d1%82%d0%b0-%d0%bf%d1%80%d0%be%d0%b5%d0%ba%d1%82-mitofusina-2-onlus\/","title":{"rendered":"\u0410\u0441\u043e\u0446\u0438\u0430\u0446\u0438\u044f\u0442\u0430 \u041f\u0440\u043e\u0435\u043a\u0442 Mitofusina 2 Onlus"},"content":{"rendered":"<div id='full_slider_1'  class='avia-fullwidth-slider main_color avia-shadow   avia-builder-el-0  el_before_av_textblock  avia-builder-el-first   container_wrap fullsize'  ><div  class='avia-slideshow av-4kl3lo-4c6c9e31f9a20811cfc5b1b7d3181743 avia-slideshow-featured av_slideshow_full avia-slide-slider av-slideshow-ui av-control-default av-slideshow-manual av-loop-once av-loop-manual-endless av-default-height-applied   avia-slideshow-1' data-slideshow-options=\"{&quot;animation&quot;:&quot;slide&quot;,&quot;autoplay&quot;:false,&quot;loop_autoplay&quot;:&quot;once&quot;,&quot;interval&quot;:5,&quot;loop_manual&quot;:&quot;manual-endless&quot;,&quot;autoplay_stopper&quot;:false,&quot;noNavigation&quot;:false,&quot;bg_slider&quot;:false,&quot;keep_padding&quot;:false,&quot;hoverpause&quot;:false,&quot;show_slide_delay&quot;:0}\"  itemprop=\"image\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/ImageObject\" ><ul class='avia-slideshow-inner ' style='padding-bottom: 28.666666666667%;'><li  class='avia-slideshow-slide av-4kl3lo-4c6c9e31f9a20811cfc5b1b7d3181743__0  av-single-slide slide-1 slide-odd'><div data-rel='slideshow-1' class='avia-slide-wrap '   ><img decoding=\"async\" fetchpriority=\"high\" class=\"wp-image-1948 avia-img-lazy-loading-not-1948\"  src=\"https:\/\/www.progettomitofusina2.com\/wp-content\/uploads\/2022\/05\/cover-lingue-1500x430-1.jpg\" width=\"1500\" height=\"430\" title='cover-lingue-1500x430' alt=''  itemprop=\"thumbnailUrl\" srcset=\"https:\/\/www.progettomitofusina2.com\/wp-content\/uploads\/2022\/05\/cover-lingue-1500x430-1.jpg 1500w, https:\/\/www.progettomitofusina2.com\/wp-content\/uploads\/2022\/05\/cover-lingue-1500x430-1-300x86.jpg 300w, https:\/\/www.progettomitofusina2.com\/wp-content\/uploads\/2022\/05\/cover-lingue-1500x430-1-1030x295.jpg 1030w, https:\/\/www.progettomitofusina2.com\/wp-content\/uploads\/2022\/05\/cover-lingue-1500x430-1-768x220.jpg 768w, https:\/\/www.progettomitofusina2.com\/wp-content\/uploads\/2022\/05\/cover-lingue-1500x430-1-705x202.jpg 705w\" sizes=\"(max-width: 1500px) 100vw, 1500px\" \/><\/div><\/li><\/ul><\/div><\/div><div id='after_full_slider_1'  class='main_color av_default_container_wrap container_wrap fullsize'  ><div class='container av-section-cont-open' ><div class='template-page content  av-content-full alpha units'><div class='post-entry post-entry-type-page post-entry-2837'><div class='entry-content-wrapper clearfix'>\n<section  class='av_textblock_section av-l3vao7di-85996eece0f524129cae4b0c1afcef95 '   itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/CreativeWork\" ><div class='avia_textblock'  itemprop=\"text\" ><p>\u0410\u0441\u043e\u0446\u0438\u0430\u0446\u0438\u044f\u0442\u0430 <strong>\u201c\u041f\u0440\u043e\u0435\u043a\u0442 Mitofusina 2 Onlus\u201d<\/strong> \u0435 \u043e\u0441\u043d\u043e\u0432\u0430\u043d\u0430 \u043e\u0442 \u0433\u0440\u0443\u043f\u0430 \u0440\u043e\u0434\u0438\u0442\u0435\u043b\u0438, \u0431\u043b\u0438\u0437\u043a\u0438 \u0438 \u043f\u0440\u0438\u044f\u0442\u0435\u043b\u0438 \u043d\u0430 \u0432\u044a\u0437\u0440\u0430\u0441\u0442\u043d\u0438 \u0438 \u043e\u0441\u043d\u043e\u0432\u043d\u043e \u043d\u0430 \u0434\u0435\u0446\u0430 \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u0438, \u0437\u0430\u0441\u0435\u0433\u043d\u0430\u0442\u0438 \u043e\u0442 \u043c\u043d\u043e\u0433\u043e \u0440\u044f\u0434\u043a\u043e \u0437\u0430\u0431\u043e\u043b\u044f\u0432\u0430\u043d\u0435: \u043f\u0435\u0440\u0438\u0444\u0435\u0440\u0438\u0439\u043d\u0430 \u043d\u0430\u0441\u043b\u0435\u0434\u0441\u0442\u0432\u0435\u043d\u0430 \u043d\u0435\u0432\u0440\u043e\u043f\u0430\u0442\u0438\u044f \u043f\u0440\u0435\u0434\u0438\u0437\u0432\u0438\u043a\u0430\u043d\u0430 \u043e\u0442 \u043c\u0443\u0442\u0430\u0446\u0438\u044f\u0442\u0430 \u043d\u0430 \u0433\u0435\u043d\u0430 Mitofusin 2 (MFN2) (<strong>HMNS2<\/strong>).<\/p>\n<p>\u041d\u0430\u0437\u0432\u0430\u043d\u0438\u0435\u0442\u043e \u0441\u0438\u043d\u0434\u0440\u043e\u043c \u043d\u0430 Charcot-Marie-Tooth \u0435 \u043f\u043e\u0437\u043d\u0430\u0442\u043e \u043a\u0430\u0442\u043e \u0440\u044f\u0434\u043a\u043e \u0437\u0430\u0431\u043e\u043b\u044f\u0432\u0430\u043d\u0435 \u0437\u0430\u0441\u044f\u0433\u0430\u0449\u043e \u043f\u0435\u0440\u0438\u0444\u0435\u0440\u0438\u0439\u043d\u0438\u0442\u0435 \u043d\u0435\u0440\u0432\u043d\u0438 \u043a\u043b\u0435\u0442\u043a\u0438, \u043a\u043e\u0438\u0442\u043e \u0441\u0430 \u043e\u0442\u0433\u043e\u0432\u043e\u0440\u043d\u0438 \u0437\u0430 \u043a\u043e\u043d\u0442\u0440\u043e\u043b\u0438\u0440\u0430\u043d\u0435\u0442\u043e \u043d\u0430 \u0434\u0432\u0438\u0433\u0430\u0442\u0435\u043b\u043d\u0438\u0442\u0435 \u0438 \u0441\u0435\u0442\u0438\u0432\u043d\u0438 \u0444\u0443\u043d\u043a\u0446\u0438\u0438, \u0438 \u0432\u043e\u0434\u0435\u0449\u043e \u0434\u043e \u0442\u0435\u0436\u043a\u043e \u043d\u0435\u0432\u0440\u043e\u043b\u043e\u0433\u0438\u0447\u043d\u043e \u0441\u043c\u0443\u0449\u0435\u043d\u0438\u0435. \u0425\u043e\u0440\u0430\u0442\u0430, \u0437\u0430\u0441\u0435\u0433\u043d\u0430\u0442\u0438 \u043e\u0442 CMT2A, \u0441\u0442\u0440\u0430\u0434\u0430\u0442 \u043e\u0442 \u0442\u0435\u0436\u043a\u0438 \u0443\u0432\u0440\u0435\u0436\u0434\u0430\u043d\u0438\u044f \u043d\u0430 \u0434\u0432\u0438\u0433\u0430\u0442\u0435\u043b\u043d\u0430\u0442\u0430 \u0430\u043a\u0442\u0438\u0432\u043d\u043e\u0441\u0442, \u043e\u0442\u0441\u043b\u0430\u0431\u0432\u0430\u043d\u0435 \u043d\u0430 \u043c\u0443\u0441\u043a\u0443\u043b\u043d\u043e\u0442\u043e \u0438 \u0434\u0440\u0443\u0433\u0438 \u0444\u0438\u0437\u0438\u0447\u0435\u0441\u043a\u0438 \u0441\u044a\u0441\u0442\u043e\u044f\u043d\u0438\u044f. \u0412 \u0440\u0435\u0437\u0443\u043b\u0442\u0430\u0442 \u043d\u0430 \u0442\u043e\u0432\u0430 \u0442\u0435 \u043f\u0440\u0435\u0441\u0442\u0430\u0432\u0430\u0442 \u0434\u0430 \u0431\u044a\u0434\u0430\u0442 \u0441\u0430\u043c\u043e\u0441\u0442\u043e\u044f\u0442\u0435\u043b\u043d\u0438.<\/p>\n<p>\u0422\u043e\u0432\u0430 \u0435 \u043d\u0435\u0438\u0437\u0432\u043b\u0438\u0447\u0430\u0449\u0430 \u0438\u0437\u0433\u043e\u0434\u0430 \u0430\u0441\u043e\u0446\u0438\u0430\u0446\u0438\u044f, \u043a\u043e\u044f\u0442\u043e \u0438\u043c\u0430 \u0437\u0430 \u0446\u0435\u043b \u0434\u0430 \u0441\u044a\u0437\u0434\u0430\u0434\u0435 \u043c\u0440\u0435\u0436\u0430 \u043e\u0442 \u0438\u0442\u0430\u043b\u0438\u0430\u043d\u0441\u043a\u0438 \u0438 \u0447\u0443\u0436\u0434\u0435\u0441\u0442\u0440\u0430\u043d\u043d\u0438 \u0441\u0435\u043c\u0435\u0439\u0441\u0442\u0432\u0430 \u043d\u0430 \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u0438 \u0437\u0430\u0441\u0435\u0433\u043d\u0430\u0442\u0438 \u043e\u0442 CMT2A, \u0434\u0430 \u043d\u0430\u0441\u044a\u0440\u0447\u0438 \u0441\u044a\u0442\u0440\u0443\u0434\u043d\u0438\u0447\u0435\u0441\u0442\u0432\u043e \u0441 \u0438\u0437\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u0442\u0435\u043b\u0438 \u0438 \u043f\u0440\u043e\u0444\u0435\u0441\u0438\u043e\u043d\u0430\u043b\u0438\u0441\u0442\u0438 \u0432 \u043e\u0431\u043b\u0430\u0441\u0442\u0442\u0430 \u043d\u0430 \u043c\u0435\u0434\u0438\u0446\u0438\u043d\u0430\u0442\u0430 \u0438 \u0434\u0430 \u043d\u0430\u0431\u0438\u0440\u0430 \u0441\u0440\u0435\u0434\u0441\u0442\u0432\u0430 \u0437\u0430 \u0440\u0430\u0437\u0440\u0430\u0431\u043e\u0442\u0432\u0430\u043d\u0435\u0442\u043e \u043d\u0430 \u043d\u0430\u0443\u0447\u043d\u0438 \u0438\u0437\u0441\u043b\u0435\u0434\u0432\u0430\u043d\u0438\u044f \u0432\u044a\u0440\u0445\u0443 CMT2A. \u0420\u0430\u0437\u043f\u043e\u043b\u0430\u0433\u0430\u043c\u0435 \u0441\u044a\u0441 \u0441\u043e\u0431\u0441\u0442\u0432\u0435\u043d\u0438 \u043d\u0430\u0443\u0447\u043d\u043e\u0438\u0437\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u0442\u0435\u043b\u0441\u043a\u0438 \u043f\u0440\u043e\u0435\u043a\u0442\u0438 \u043f\u043e\u0441\u0432\u0435\u0442\u0435\u043d\u0438 \u043d\u0430 \u043b\u0435\u0447\u0435\u043d\u0438\u0435\u0442\u043e \u043d\u0430 CMT2A \u0438 \u043f\u043e-\u0441\u043f\u0435\u0446\u0438\u0430\u043b\u043d\u043e \u043d\u0430\u0448\u0438\u044f\u0442 \u043f\u0440\u043e\u0435\u043a\u0442 \u201e\u0420\u0430\u0437\u0440\u0430\u0431\u043e\u0442\u043a\u0430 \u043d\u0430 \u043c\u0435\u0442\u043e\u0434 \u043e\u0441\u043d\u043e\u0432\u0430\u043d \u043d\u0430 \u0441\u0442\u0432\u043e\u043b\u043e\u0432\u0438 \u043a\u043b\u0435\u0442\u043a\u0438 \u0437\u0430 \u043b\u0435\u0447\u0435\u043d\u0438\u0435\u0442\u043e \u043d\u0430 \u0431\u043e\u043b\u0435\u0441\u0442\u0442\u0430 cmt \u0441\u0432\u044a\u0440\u0437\u0430\u043d\u0430 \u0441 \u043c\u0443\u0442\u0430\u0446\u0438\u044f\u0442\u0430 \u043d\u0430 \u0433\u0435\u043d\u0430 Mitofusin 2 (CMT2A)\u201d.<\/p>\n<p>\u0422\u043e\u0432\u0430 \u0435 \u0435\u0434\u0438\u043d\u0441\u0442\u0432\u0435\u043d\u0438\u044f\u0442 \u0437\u0430\u0441\u0435\u0433\u0430 \u0434\u0435\u0439\u0441\u0442\u0432\u0430\u0449 \u043d\u0430\u0443\u0447\u0435\u043d \u043f\u0440\u043e\u0435\u043a\u0442 \u0437\u0430 \u0438\u0434\u0435\u043d\u0442\u0438\u0444\u0438\u0446\u0438\u0440\u0430\u043d\u0435 \u043d\u0430 \u0437\u0430\u0431\u043e\u043b\u044f\u0432\u0430\u043d\u0435\u0442\u043e \u0441\u0432\u044a\u0440\u0437\u0430\u043d\u043e \u0441 \u043c\u0443\u0442\u0430\u0446\u0438\u044f\u0442\u0430 \u043d\u0430 \u0433\u0435\u043d\u0430 Mitofusin 2. \u0422\u043e\u0439 \u0441\u0435 \u043f\u0440\u043e\u0432\u0435\u0436\u0434\u0430 \u043e\u0442 \u041a\u0430\u0442\u0435\u0434\u0440\u0430\u0442\u0430 \u043f\u043e \u043d\u0435\u0432\u0440\u043e\u043b\u043e\u0433\u0438\u0447\u043d\u0438 \u043d\u0430\u0443\u043a\u0438 \u043a\u044a\u043c \u0423\u043d\u0438\u0432\u0435\u0440\u0441\u0438\u0442\u0435\u0442\u0430 \u0432 \u041c\u0438\u043b\u0430\u043d\u043e \u0438 \u0441\u0435 \u0440\u044a\u043a\u043e\u0432\u043e\u0434\u0438 \u043e\u0442 \u043f\u0440\u043e\u0444. \u0414\u0436\u0430\u043a\u043e\u043c\u043e \u041a\u043e\u043c\u0438.<\/p>\n<p>\u0410\u0441\u043e\u0446\u0438\u044f\u0446\u0438\u044f\u0442\u0430 \u0438\u043c\u0430 \u0441\u044a\u0449\u043e \u0432\u044a\u0437\u043c\u043e\u0436\u043d\u043e\u0441\u0442 \u0434\u0430 \u043e\u0440\u0433\u0430\u043d\u0438\u0437\u0438\u0440\u0430 \u0438 \u043d\u0430\u0441\u044a\u0440\u0447\u0430\u0432\u0430 \u0441\u044a\u0431\u0438\u0442\u0438\u044f, \u043a\u043e\u043d\u0444\u0435\u0440\u0435\u043d\u0446\u0438\u0438 \u0438 \u0441\u0440\u0435\u0449\u0438 \u0437\u0430 \u043f\u043e\u0432\u0434\u0438\u0433\u0430\u043d\u0435 \u043d\u0430 \u043e\u0431\u0449\u0435\u0441\u0442\u0432\u0435\u043d\u0438\u044f \u0438\u043d\u0442\u0435\u0440\u0435\u0441 \u043e\u0442 \u0442\u043e\u0432\u0430 \u0440\u044f\u0434\u043a\u043e \u0437\u0430\u0431\u043e\u043b\u044f\u0432\u0430\u043d\u0435. \u0410\u043a\u043e \u0412\u0438\u0435 \u0443\u0441\u0435\u0449\u0430\u0442\u0435 \u0441\u0438\u043c\u043f\u0442\u043e\u043c\u0438 \u043f\u043e\u0434\u043e\u0431\u043d\u0438 \u043d\u0430 \u043e\u043f\u0438\u0441\u0430\u043d\u0438\u0442\u0435 \u043f\u043e-\u0433\u043e\u0440\u0435, \u043d\u043e \u043d\u0435 \u0437\u043d\u0430\u0435\u0442\u0435 \u043e\u0442 \u043a\u0430\u043a\u0432\u043e \u0437\u0430\u0431\u043e\u043b\u044f\u0432\u0430\u043d\u0435 \u0441\u0442\u0440\u0430\u0434\u0430\u0442\u0435 \u0438\u043b\u0438 \u0430\u043a\u043e \u043f\u043e\u0437\u043d\u0430\u0432\u0430\u0442\u0435 \u043d\u044f\u043a\u043e\u0433\u043e \u0441\u0442\u0440\u0430\u0434\u0430\u0449 \u043e\u0442 \u043f\u043e\u0434\u043e\u0431\u043d\u0438 \u043d\u0435\u0449\u0430, \u043d\u043e \u0432\u0441\u0435 \u043e\u0449\u0435 \u043d\u0435 \u043d\u0430\u043c\u0435\u0440\u0438\u043b \u043e\u0442\u0433\u043e\u0432\u043e\u0440 \u043d\u0430 \u043f\u0440\u043e\u0431\u043b\u0435\u043c\u0438\u0442\u0435 \u0441\u0438, \u043d\u0430\u043f\u0438\u0448\u0435\u0442\u0435 \u043d\u0438 \u043d\u0430 \u0430\u0434\u0440\u0435\u0441 \u043d\u0430 \u0435\u043b\u043a\u0442\u0440\u043e\u043d\u043d\u0430 \u043f\u043e\u0449\u0430: <a href=\"mailto:info@progettomitofusina2.com\">info@progettomitofusina2.com<\/a><\/p>\n<\/div><\/section>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":0,"parent":2737,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-2837","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/pages\/2837","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/comments?post=2837"}],"version-history":[{"count":2,"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/pages\/2837\/revisions"}],"predecessor-version":[{"id":2839,"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/pages\/2837\/revisions\/2839"}],"up":[{"embeddable":true,"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/pages\/2737"}],"wp:attachment":[{"href":"https:\/\/www.progettomitofusina2.com\/en\/wp-json\/wp\/v2\/media?parent=2837"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}